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Query OMIM entry list
250620
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BETA-HYDROXYISOBUTYRYL CoA DEACYLASE, DEFICIENCY OF
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Organic Chemicals
Amines
Ethylamines
Mercaptoethylamines
Cysteamine
Sulfur Compounds
Amino Acids, Sulfur
Cysteine
Sulfhydryl Compounds
Cysteine
Mercaptoethylamines
Cysteamine
Heterocyclic Compounds
Heterocyclic Compounds, 2-Ring
Purines
Purine Nucleotides
Adenine Nucleotides
Coenzyme A
Acyl Coenzyme A
Enzymes and Coenzymes
Coenzymes
Coenzyme A
Acyl Coenzyme A
Enzymes
Hydrolases
Esterases
Thiolester Hydrolases
Lyases
Carbon-Oxygen Lyases
Hydro-Lyases
Enoyl-CoA Hydratase
Amino Acids, Peptides, and Proteins
Amino Acids
Amino Acids, Branched-Chain
Valine
Amino Acids, Essential
Valine
Amino Acids, Neutral
Cysteine
Amino Acids, Sulfur
Cysteine
Nucleic Acids, Nucleotides, and Nucleosides
Nucleotides
Purine Nucleotides
Adenine Nucleotides
Coenzyme A
Acyl Coenzyme A
Ribonucleotides
Adenine Nucleotides
Coenzyme A
Acyl Coenzyme A
Database Center for Life Science