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251000
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METHYLMALONIC ACIDURIA DUE TO METHYLMALONYL-CoA MUTASE DEFICIENCY
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Inorganic Chemicals
Alkalies
Carbon Compounds, Inorganic
Carbon Dioxide
Gases
Carbon Dioxide
Hydrogen
Tritium
Isotopes
Carbon Isotopes
Radioisotopes
Tritium
Oxygen Compounds
Oxides
Carbon Dioxide
Organic Chemicals
Alcohols
Glycols
Ethylene Glycols
Ethylene Glycol
Carboxylic Acids
Acids, Acyclic
Dicarboxylic Acids
Malonates
Methylmalonic Acid
Succinates
Propionates
Keto Acids
Ketones
Ketone Bodies
Sulfur Compounds
Amino Acids, Sulfur
Methionine
Urea
Heterocyclic Compounds
Acids, Heterocyclic
Xanthurenates
Heterocyclic Compounds, 1-Ring
Azoles
Imidazoles
Creatinine
Pyrroles
Tetrapyrroles
Corrinoids
Vitamin B 12
Cobamides
Hydroxocobalamin
Pyridines
Picolines
Vitamin B 6
Pyridoxal
Pyridoxal Phosphate
Heterocyclic Compounds, 2-Ring
Purines
Purine Nucleotides
Adenine Nucleotides
Coenzyme A
Acyl Coenzyme A
Heterocyclic Compounds with 4 or More Rings
Tetrapyrroles
Corrinoids
Vitamin B 12
Cobamides
Hydroxocobalamin
Polycyclic Compounds
Macrocyclic Compounds
Tetrapyrroles
Corrinoids
Vitamin B 12
Cobamides
Hydroxocobalamin
Enzymes and Coenzymes
Coenzymes
Cobamides
Coenzyme A
Acyl Coenzyme A
Pyridoxal Phosphate
Enzymes
Holoenzymes
Apoenzymes
Isomerases
Intramolecular Transferases
Methylmalonyl-CoA Mutase
Ligases
Lyases
Carbon-Oxygen Lyases
Hydro-Lyases
Lipids
Fatty Acids
Fatty Acids, Volatile
Propionates
Amino Acids, Peptides, and Proteins
Amino Acids
Amino Acids, Basic
Asparagine
Amino Acids, Branched-Chain
Isoleucine
Leucine
Valine
Amino Acids, Cyclic
Amino Acids, Aromatic
Tyrosine
Amino Acids, Diamino
Asparagine
Amino Acids, Essential
Isoleucine
Leucine
Methionine
Threonine
Valine
Amino Acids, Neutral
Asparagine
Methionine
Threonine
Amino Acids, Sulfur
Methionine
Glycine
Threonine
Peptides
Protein Sorting Signals
Proteins
Apoproteins
Apoenzymes
Dietary Proteins
Nucleic Acids, Nucleotides, and Nucleosides
Nucleic Acids
DNA
Nucleic Acid Probes
Oligonucleotide Probes
RNA
RNA, Messenger
Codon
Codon, Terminator
Codon, Nonsense
RNA Splice Sites
Nucleotides
Purine Nucleotides
Adenine Nucleotides
Coenzyme A
Acyl Coenzyme A
Ribonucleotides
Adenine Nucleotides
Coenzyme A
Acyl Coenzyme A
Complex Mixtures
Tissue Extracts
Chemical Actions and Uses
Specialty Uses of Chemicals
Laboratory Chemicals
Molecular Probes
Nucleic Acid Probes
Oligonucleotide Probes
Database Center for Life Science