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Query OMIM entry list
211600
PFIC1
CHOLESTASIS, PROGRESSIVE FAMILIAL INTRAHEPATIC 1
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Inorganic Chemicals
Chlorine Compounds
Hydrochloric Acid
Chlorides
Electrolytes
Ions
Anions
Chlorides
Elements
Metals, Alkaline Earth
Calcium
Metals
Metals, Alkaline Earth
Calcium
Organic Chemicals
Hydrocarbons
Hydrocarbons, Cyclic
Hydrocarbons, Aromatic
Benzene Derivatives
Phenols
Phenolphthaleins
Sulfobromophthalein
Polycyclic Hydrocarbons, Aromatic
Spiro Compounds
Fluoresceins
Rose Bengal
Heterocyclic Compounds
Heterocyclic Compounds, 1-Ring
Azoles
Pyrroles
Tetrapyrroles
Bile Pigments
Bilirubin
Pyrimidines
Pyrimidinones
Barbiturates
Phenobarbital
Heterocyclic Compounds, 2-Ring
Benzopyrans
Vitamin E
Indoles
Naphthyridines
Purines
Purine Nucleotides
Adenine Nucleotides
Cyclic AMP
Heterocyclic Compounds, 3-Ring
Xanthenes
Fluoresceins
Rose Bengal
Heterocyclic Compounds with 4 or More Rings
Tetrapyrroles
Bile Pigments
Bilirubin
Pyrans
Benzopyrans
Vitamin E
Polycyclic Compounds
Macrocyclic Compounds
Tetrapyrroles
Bile Pigments
Bilirubin
Polycyclic Hydrocarbons, Aromatic
Spiro Compounds
Fluoresceins
Rose Bengal
Steroids
Bile Acids and Salts
Cholic Acids
Deoxycholic Acid
Chenodeoxycholic Acid
Cholanes
Cholic Acids
Deoxycholic Acid
Chenodeoxycholic Acid
Cholestanes
Cholestenes
Cholesterol
Sterols
Cholesterol
Secosteroids
Vitamin D
Macromolecular Substances
Polymers
Plastics
Polystyrenes
Cholestyramine Resin
Hormones, Hormone Substitutes, and Hormone Antagonists
Hormones
Peptide Hormones
Parathyroid Hormone
Enzymes and Coenzymes
Enzyme Precursors
Prothrombin
Enzymes
Hydrolases
Acid Anhydride Hydrolases
Adenosine Triphosphatases
Esterases
Phosphoric Monoester Hydrolases
Alkaline Phosphatase
Transferases
Acyltransferases
Aminoacyltransferases
gamma-Glutamyltransferase
Nitrogenous Group Transferases
Transaminases
Alanine Transaminase
Aspartate Aminotransferases
Lipids
Glycerides
Triglycerides
Lipofuscin
Membrane Lipids
Sterols
Cholesterol
Sterols
Cholesterol
Amino Acids, Peptides, and Proteins
Peptides
Intercellular Signaling Peptides and Proteins
Cytokines
Peptide Fragments
Peptide Hormones
Parathyroid Hormone
Proteins
Albumins
Serum Albumin
Blood Proteins
Acute-Phase Proteins
Serum Albumin
Blood Coagulation Factors
Prothrombin
Serum Albumin
Serum Globulins
Alpha-Globulins
Beta-Globulins
Carrier Proteins
Calcium-Binding Proteins
Osteocalcin
Membrane Transport Proteins
Ion Pumps
Globulins
Serum Globulins
Alpha-Globulins
Beta-Globulins
Intercellular Signaling Peptides and Proteins
Cytokines
Membrane Proteins
Membrane Transport Proteins
Ion Pumps
Protein Precursors
Procollagen
Scleroproteins
Extracellular Matrix Proteins
Collagen
Procollagen
Nucleic Acids, Nucleotides, and Nucleosides
Nucleotides
Nucleotides, Cyclic
Cyclic AMP
Purine Nucleotides
Adenine Nucleotides
Cyclic AMP
Ribonucleotides
Adenine Nucleotides
Cyclic AMP
Biological Factors
Antigens
Antigens, Surface
Blood Group Antigens
Isoantigens
Blood Group Antigens
Biological Markers
Genetic Markers
Blood Coagulation Factors
Calcium
Prothrombin
Intercellular Signaling Peptides and Proteins
Cytokines
Pigments, Biological
Bile Pigments
Bilirubin
Lipofuscin
Biomedical and Dental Materials
Polymers
Plastics
Polystyrenes
Cholestyramine Resin
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