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236250
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HOMOCYSTINURIA DUE TO DEFICIENCY OF N(5,10)-METHYLENETETRAHYDROFOLATE REDUCTASE ACTIVITY
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Inorganic Chemicals
Isotopes
Carbon Isotopes
Organic Chemicals
Amines
Biogenic Amines
Quaternary Ammonium Compounds
Trimethyl Ammonium Compounds
Betaine
Onium Compounds
Quaternary Ammonium Compounds
Betaine
Sulfur Compounds
Amino Acids, Sulfur
Homocysteine
Homocystine
Methionine
S-Adenosylmethionine
Heterocyclic Compounds
Heterocyclic Compounds, 1-Ring
Azoles
Pyrroles
Tetrapyrroles
Corrinoids
Vitamin B 12
Pyridines
Picolines
Vitamin B 6
Pyridoxine
Pyrimidines
Pyrimidinones
Cytosine
Uracil
Thymine
Heterocyclic Compounds, 2-Ring
Pteridines
Flavins
Riboflavin
Flavin-Adenine Dinucleotide
Pterins
Biopterin
Folic Acid
Tetrahydrofolates
Formyltetrahydrofolates
Leucovorin
Purines
Adenine
Purine Nucleosides
Adenosine
S-Adenosylmethionine
Purine Nucleotides
Adenine Nucleotides
Flavin-Adenine Dinucleotide
Heterocyclic Compounds, 3-Ring
Flavins
Riboflavin
Flavin-Adenine Dinucleotide
Heterocyclic Compounds with 4 or More Rings
Tetrapyrroles
Corrinoids
Vitamin B 12
Polycyclic Compounds
Macrocyclic Compounds
Tetrapyrroles
Corrinoids
Vitamin B 12
Enzymes and Coenzymes
Coenzymes
Biopterin
Flavins
Riboflavin
Flavin-Adenine Dinucleotide
Tetrahydrofolates
Formyltetrahydrofolates
Leucovorin
Enzymes
Hydrolases
Aminohydrolases
Methenyltetrahydrofolate Cyclohydrolase
Ligases
Carbon-Nitrogen Ligases
Formate-Tetrahydrofolate Ligase
Lyases
Carbon-Nitrogen Lyases
Ammonia-Lyases
L-Serine Dehydratase
Carbon-Oxygen Lyases
Hydro-Lyases
Cystathionine beta-Synthase
Oxidoreductases
Alcohol Oxidoreductases
Carbohydrate Dehydrogenases
Sugar Alcohol Dehydrogenases
Glycerolphosphate Dehydrogenase
5,10-Methylenetetrahydrofolate Reductase (FADH2)
Oxidoreductases Acting on CH-NH Group Donors
Methylenetetrahydrofolate Dehydrogenase (NAD+)
Methylenetetrahydrofolate Dehydrogenase (NADP)
Methylenetetrahydrofolate Reductase (NADPH2)
Tetrahydrofolate Dehydrogenase
Oxidoreductases Acting on Sulfur Group Donors
Ferredoxin-NADP Reductase
Transferases
One-Carbon Group Transferases
Methyltransferases
5-Methyltetrahydrofolate-Homocysteine S-Methyltransferase
Amino Acids, Peptides, and Proteins
Amino Acids
Alanine
Amino Acids, Branched-Chain
Valine
Amino Acids, Diamino
Homocystine
Amino Acids, Dicarboxylic
Homocystine
Amino Acids, Essential
Methionine
Valine
Amino Acids, Neutral
Methionine
Amino Acids, Sulfur
Homocysteine
Homocystine
Methionine
S-Adenosylmethionine
Proteins
Bacterial Proteins
Flavoproteins
Methylenetetrahydrofolate Reductase (NADPH2)
Recombinant Proteins
Nucleic Acids, Nucleotides, and Nucleosides
Nucleic Acids
DNA
DNA, Recombinant
DNA, Single-Stranded
DNA, Complementary
Nucleic Acid Probes
DNA Probes
DNA, Complementary
Nucleosides
Purine Nucleosides
Adenosine
S-Adenosylmethionine
Ribonucleosides
Adenosine
S-Adenosylmethionine
Nucleotides
Polynucleotides
Oligonucleotides
Oligodeoxyribonucleotides
DNA Primers
Purine Nucleotides
Adenine Nucleotides
Flavin-Adenine Dinucleotide
Ribonucleotides
Adenine Nucleotides
Flavin-Adenine Dinucleotide
Biological Factors
Pigments, Biological
Flavins
Riboflavin
Flavin-Adenine Dinucleotide
Chemical Actions and Uses
Pharmacologic Actions
Physiological Effects of Drugs
Growth Substances
Micronutrients
Vitamins
Vitamin B Complex
Specialty Uses of Chemicals
Laboratory Chemicals
Molecular Probes
Nucleic Acid Probes
DNA Probes
DNA, Complementary
DNA Primers
Database Center for Life Science