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Query OMIM entry list
237300
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CARBAMOYL PHOSPHATE SYNTHETASE I DEFICIENCY, HYPERAMMONEMIA DUE TO
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Inorganic Chemicals
Elements
Nitrogen
Gases
Ammonia
Nitrogen
Nitrogen Compounds
Ammonia
Organic Chemicals
Carboxylic Acids
Acids, Acyclic
Carbamates
Propionates
Valerates
Pentanoic Acids
Valproic Acid
Acids, Carbocyclic
Benzoates
Benzoic Acid
Phenylacetates
Keto Acids
Hydrocarbons
Hydrocarbons, Cyclic
Hydrocarbons, Aromatic
Benzene Derivatives
Benzoates
Benzoic Acid
Sulfur Compounds
Amino Acids, Sulfur
Methionine
Urea
Heterocyclic Compounds
Heterocyclic Compounds, 1-Ring
Azoles
Imidazoles
Imidazolidines
Hydantoins
Phenytoin
Hormones, Hormone Substitutes, and Hormone Antagonists
Hormones
Peptide Hormones
Pancreatic Hormones
Insulins
Proinsulin
Insulin
Enzymes and Coenzymes
Enzymes
Hydrolases
Ureohydrolases
Arginase
Ligases
Carbon-Nitrogen Ligases
Argininosuccinate Synthase
Carbamoyl-Phosphate Synthase (Ammonia)
Lyases
Carbon-Nitrogen Lyases
Amidine-Lyases
Argininosuccinate Lyase
Transferases
Nitrogenous Group Transferases
Transaminases
Ornithine-Oxo-Acid Transaminase
One-Carbon Group Transferases
Carboxyl and Carbamoyl Transferases
Ornithine Carbamoyltransferase
Phosphotransferases
Phosphotransferases (Alcohol Group Acceptor)
Glucokinase
Lipids
Fatty Acids
Fatty Acids, Volatile
Propionates
Valerates
Pentanoic Acids
Valproic Acid
Amino Acids, Peptides, and Proteins
Amino Acids
Amino Acids, Acidic
Glutamic Acid
Glutamates
Amino Acids, Basic
Arginine
Glutamine
Ornithine
Amino Acids, Branched-Chain
Isoleucine
Leucine
Valine
Amino Acids, Cyclic
Amino Acids, Aromatic
Phenylalanine
Imino Acids
Proline
Amino Acids, Diamino
Arginine
Citrulline
Glutamine
Ornithine
Amino Acids, Dicarboxylic
Glutamic Acid
Glutamates
Amino Acids, Essential
Arginine
Isoleucine
Leucine
Methionine
Phenylalanine
Valine
Amino Acids, Neutral
Glutamine
Methionine
Amino Acids, Sulfur
Methionine
Glycine
Peptides
Peptide Hormones
Pancreatic Hormones
Insulins
Proinsulin
Insulin
Nucleic Acids, Nucleotides, and Nucleosides
Nucleic Acids
DNA
RNA
RNA, Messenger
Nucleotides
Polynucleotides
Oligonucleotides
Oligodeoxyribonucleotides
DNA Primers
Chemical Actions and Uses
Specialty Uses of Chemicals
Laboratory Chemicals
Molecular Probes
Nucleic Acid Probes
DNA Probes
DNA Primers
Database Center for Life Science