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245348
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PYRUVATE DEHYDROGENASE E2 DEFICIENCY
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Macromolecular Substances
Multiprotein Complexes
Multienzyme Complexes
Pyruvate Dehydrogenase Complex
Dihydrolipoyllysine-Residue Acetyltransferase
Enzymes and Coenzymes
Enzymes
Multienzyme Complexes
Pyruvate Dehydrogenase Complex
Dihydrolipoyllysine-Residue Acetyltransferase
Transferases
Acyltransferases
Acetyltransferases
Dihydrolipoyllysine-Residue Acetyltransferase
Amino Acids, Peptides, and Proteins
Amino Acids
Amino Acids, Acidic
Glutamic Acid
Amino Acids, Branched-Chain
Leucine
Amino Acids, Cyclic
Amino Acids, Aromatic
Phenylalanine
Amino Acids, Dicarboxylic
Glutamic Acid
Amino Acids, Essential
Leucine
Phenylalanine
Excitatory Amino Acids
Glutamic Acid
Peptides
Proteins
Mitochondrial Proteins
Biological Factors
Antigens
Autoantigens
Database Center for Life Science