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Query OMIM entry list
246450
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3-@HYDROXY-3-METHYLGLUTARYL-CoA LYASE DEFICIENCY
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Inorganic Chemicals
Carbon Compounds, Inorganic
Carbonic Acid
Carbonates
Bicarbonates
Electrolytes
Ions
Anions
Carbonates
Bicarbonates
Organic Chemicals
Amines
Quaternary Ammonium Compounds
Trimethyl Ammonium Compounds
Carnitine
Carboxylic Acids
Acids, Acyclic
Butyrates
Crotonates
Hydroxybutyrates
Dicarboxylic Acids
Glutarates
Meglutol
Valerates
Hydroxy Acids
3-Hydroxybutyric Acid
Hydroxybutyrates
Lactates
Ketones
Ketone Bodies
Heterocyclic Compounds
Heterocyclic Compounds, 1-Ring
Azoles
Imidazoles
Creatinine
Heterocyclic Compounds, 2-Ring
Purines
Purine Nucleotides
Adenine Nucleotides
Coenzyme A
Acyl Coenzyme A
Enzymes and Coenzymes
Coenzymes
Coenzyme A
Acyl Coenzyme A
Enzymes
Lyases
Carbon-Carbon Lyases
Oxo-Acid-Lyases
Transferases
Acyltransferases
Hydroxymethylglutaryl-CoA Synthase
Nitrogenous Group Transferases
Transaminases
Aspartate Aminotransferases
Carbohydrates
Dietary Carbohydrates
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Hexoses
Glucose
Blood Glucose
Lipids
Fatty Acids
Fatty Acids, Volatile
Butyrates
Crotonates
Hydroxybutyrates
Valerates
Amino Acids, Peptides, and Proteins
Amino Acids
Amino Acids, Branched-Chain
Leucine
Amino Acids, Essential
Leucine
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Nucleic Acids
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Nucleic Acid Probes
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RNA
RNA, Messenger
Codon
Nucleotides
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Oligodeoxyribonucleotides
DNA Primers
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Poly A
Purine Nucleotides
Adenine Nucleotides
Coenzyme A
Acyl Coenzyme A
Ribonucleotides
Adenine Nucleotides
Coenzyme A
Acyl Coenzyme A
Chemical Actions and Uses
Specialty Uses of Chemicals
Laboratory Chemicals
Molecular Probes
Nucleic Acid Probes
DNA Probes
DNA Primers
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