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248600
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MAPLE SYRUP URINE DISEASE
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Inorganic Chemicals
Acids
Carbon Compounds, Inorganic
Carbon Dioxide
Elements
Metals, Alkali
Sodium
Gases
Carbon Dioxide
Isotopes
Carbon Isotopes
Carbon Radioisotopes
Radioisotopes
Carbon Radioisotopes
Metals
Metals, Alkali
Sodium
Oxygen Compounds
Oxides
Carbon Dioxide
Organic Chemicals
Alcohols
Sugar Alcohols
Mannitol
Amides
Sulfonamides
Sulfanilamides
Furosemide
Amines
Aniline Compounds
Sulfanilamides
Furosemide
Methylamines
Quaternary Ammonium Compounds
Trimethyl Ammonium Compounds
Carnitine
Carboxylic Acids
Acids, Acyclic
Caproates
Dicarboxylic Acids
Glutarates
Ketoglutaric Acids
Succinates
Tricarboxylic Acids
Citrates
Citric Acid
Valerates
Hydroxy Acids
Lactates
Lactic Acid
Keto Acids
Ketoglutaric Acids
Pyruvates
Hydrazines
Ketones
Nitroso Compounds
Nitrosourea Compounds
Ethylnitrosourea
Sulfur Compounds
Amino Acids, Sulfur
Cystathionine
Cysteine
Methionine
Sulfhydryl Compounds
Cysteine
Sulfones
Sulfonamides
Sulfanilamides
Furosemide
Thiazoles
Thiamine
Fursultiamin
Thiamine Pyrophosphate
Urea
Nitrosourea Compounds
Ethylnitrosourea
Heterocyclic Compounds
Alkaloids
Xanthines
Uric Acid
Heterocyclic Compounds, 1-Ring
Azoles
Imidazoles
Creatinine
Thiazoles
Thiamine
Fursultiamin
Thiamine Pyrophosphate
Furans
Pyrimidines
Fursultiamin
Pyrimidinones
Barbiturates
Phenobarbital
Uracil
Thymine
Thiamine
Fursultiamin
Thiamine Pyrophosphate
Heterocyclic Compounds, 2-Ring
Purines
Adenine
Purine Nucleotides
Adenine Nucleotides
Coenzyme A
NAD
Purinones
Xanthines
Uric Acid
Macromolecular Substances
Multiprotein Complexes
Multienzyme Complexes
Glycine Decarboxylase Complex
Dihydrolipoamide Dehydrogenase
Ketoglutarate Dehydrogenase Complex
Dihydrolipoamide Dehydrogenase
Pyruvate Dehydrogenase Complex
Dihydrolipoamide Dehydrogenase
Enzymes and Coenzymes
Coenzymes
Coenzyme A
NAD
Thiamine Pyrophosphate
Enzymes
Hydrolases
Peptide Hydrolases
Endopeptidases
Serine Endopeptidases
Trypsin
Serine Proteases
Serine Endopeptidases
Trypsin
Ligases
Carbon-Carbon Ligases
Pyruvate Carboxylase
Lyases
Carbon-Carbon Lyases
Carboxy-Lyases
Phosphoenolpyruvate Carboxykinase (GTP)
Pyruvate Decarboxylase
Multienzyme Complexes
Glycine Decarboxylase Complex
Dihydrolipoamide Dehydrogenase
Ketoglutarate Dehydrogenase Complex
Dihydrolipoamide Dehydrogenase
Pyruvate Dehydrogenase Complex
Dihydrolipoamide Dehydrogenase
Oxidoreductases
Oxidoreductases Acting on Aldehyde or Oxo Group Donors
Ketone Oxidoreductases
Ketoglutarate Dehydrogenase Complex
Dihydrolipoamide Dehydrogenase
3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)
Oxidoreductases Acting on Sulfur Group Donors
Dihydrolipoamide Dehydrogenase
Transferases
Acyltransferases
Citrate (si)-Synthase
Nitrogenous Group Transferases
Transaminases
Carbohydrates
Dietary Carbohydrates
Sugar Alcohols
Mannitol
Lipids
Fatty Acids
Fatty Acids, Volatile
Caproates
Valerates
Amino Acids, Peptides, and Proteins
Amino Acids
Alanine
Amino Acids, Basic
Arginine
Amino Acids, Branched-Chain
Isoleucine
Leucine
Valine
Amino Acids, Cyclic
Amino Acids, Aromatic
Phenylalanine
Tyrosine
Histidine
Amino Acids, Diamino
Arginine
Cystathionine
Amino Acids, Dicarboxylic
Cystathionine
Amino Acids, Essential
Arginine
Histidine
Isoleucine
Leucine
Methionine
Phenylalanine
Valine
Amino Acids, Neutral
Cysteine
Methionine
Amino Acids, Sulfur
Cystathionine
Cysteine
Methionine
Peptides
Protein Sorting Signals
Proteins
Carrier Proteins
Membrane Transport Proteins
Ion Channels
Potassium Channels
Potassium Channels, Voltage-Gated
Dietary Proteins
Flavoproteins
Dihydrolipoamide Dehydrogenase
Membrane Proteins
Membrane Glycoproteins
Ion Channels
Potassium Channels
Potassium Channels, Voltage-Gated
Membrane Transport Proteins
Ion Channels
Potassium Channels
Potassium Channels, Voltage-Gated
Protein Subunits
Recombinant Proteins
Nucleic Acids, Nucleotides, and Nucleosides
Antisense Elements (Genetics)
Nucleic Acids
DNA
DNA, Single-Stranded
DNA, Complementary
DNA Transposable Elements
Nucleic Acid Probes
Antisense Elements (Genetics)
DNA Probes
DNA, Complementary
Oligonucleotide Probes
RNA
RNA, Messenger
RNA Splice Sites
Nucleotides
Polynucleotides
Oligonucleotides
Oligodeoxyribonucleotides
DNA Primers
Purine Nucleotides
Adenine Nucleotides
Coenzyme A
NAD
Ribonucleotides
Adenine Nucleotides
Coenzyme A
NAD
Complex Mixtures
Biological Agents
Plant Preparations
Plant Extracts
Pharmaceutical Preparations
Plant Extracts
Solutions
Hypertonic Solutions
Saline Solution, Hypertonic
Chemical Actions and Uses
Specialty Uses of Chemicals
Laboratory Chemicals
Culture Media
Molecular Probes
Nucleic Acid Probes
Antisense Elements (Genetics)
DNA Probes
DNA, Complementary
DNA Primers
Oligonucleotide Probes
Toxic Actions
Noxae
Mutagens
Database Center for Life Science