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PYRUVATE CARBOXYLASE DEFICIENCY
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Inorganic Chemicals
Gases
Ammonia
Nitrogen Compounds
Ammonia
Organic Chemicals
Carboxylic Acids
Acids, Acyclic
Butyrates
Hydroxybutyrates
Hydroxy Acids
3-Hydroxybutyric Acid
Hydroxybutyrates
Lactates
Lactic Acid
Keto Acids
Acetoacetates
Pyruvates
Pyruvic Acid
Thioctic Acid
Ketones
Ketone Bodies
Acetoacetates
Sulfur Compounds
Thiazoles
Thiamine
Thiophenes
Thioctic Acid
Heterocyclic Compounds
Heterocyclic Compounds, 1-Ring
Azoles
Imidazoles
Biotin
Thiazoles
Thiamine
Pyrimidines
Thiamine
Heterocyclic Compounds, 2-Ring
Pteridines
Pterins
Folic Acid
Macromolecular Substances
Multiprotein Complexes
Multienzyme Complexes
Pyruvate Dehydrogenase Complex
Enzymes and Coenzymes
Coenzymes
Biotin
Thioctic Acid
Enzymes
Hydrolases
Esterases
Phosphoric Monoester Hydrolases
Fructose-Bisphosphatase
Ligases
Carbon-Carbon Ligases
Pyruvate Carboxylase
Lyases
Carbon-Carbon Lyases
Carboxy-Lyases
Phosphoenolpyruvate Carboxykinase (GTP)
Pyruvate Decarboxylase
Multienzyme Complexes
Pyruvate Dehydrogenase Complex
Transferases
Acyltransferases
Citrate (si)-Synthase
Carbohydrates
Monosaccharides
Hexoses
Glucose
Lipids
Fatty Acids
Fatty Acids, Volatile
Butyrates
Hydroxybutyrates
Thioctic Acid
Amino Acids, Peptides, and Proteins
Amino Acids
Alanine
Amino Acids, Diamino
Citrulline
Proteins
Bacterial Proteins
Streptavidin
Nucleic Acids, Nucleotides, and Nucleosides
Nucleic Acids
DNA
Nucleic Acid Probes
Oligonucleotide Probes
RNA
RNA, Messenger
Biological Factors
Biological Markers
Genetic Markers
Chemical Actions and Uses
Pharmacologic Actions
Therapeutic Uses
Hematologic Agents
Hematinics
Specialty Uses of Chemicals
Laboratory Chemicals
Molecular Probes
Nucleic Acid Probes
Oligonucleotide Probes
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