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268800
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SANDHOFF DISEASE
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Organic Chemicals
Alcohols
Glycols
Ethylene Glycols
Polyethylene Glycols
Amides
Ceramides
Carboxylic Acids
Acids, Acyclic
Sugar Acids
Neuraminic Acids
Sialic Acids
Uronic Acids
Acids, Aldehydic
Uronic Acids
Hydroxy Acids
Sugar Acids
Neuraminic Acids
Sialic Acids
Uronic Acids
Imines
Imino Sugars
Imino Pyranoses
1-Deoxynojirimycin
Heterocyclic Compounds
Alkaloids
1-Deoxynojirimycin
Heterocyclic Compounds, 1-Ring
Piperidines
Imino Pyranoses
1-Deoxynojirimycin
Polycyclic Compounds
Steroids
Cholestanes
Cholestenes
Cholesterol
Sterols
Cholesterol
Macromolecular Substances
Polymers
Polyethylene Glycols
Enzymes and Coenzymes
Enzymes
DNA Restriction-Modification Enzymes
DNA Restriction Enzymes
Deoxyribonucleases, Type II Site-Specific
Deoxyribonuclease HindIII
Hydrolases
Aminohydrolases
Esterases
Deoxyribonucleases
Endodeoxyribonucleases
DNA Restriction Enzymes
Deoxyribonucleases, Type II Site-Specific
Deoxyribonuclease HindIII
Endonucleases
Endodeoxyribonucleases
DNA Restriction Enzymes
Deoxyribonucleases, Type II Site-Specific
Deoxyribonuclease HindIII
Glycoside Hydrolases
Glucosidases
alpha-Glucosidases
Hexosaminidases
beta-N-Acetylhexosaminidases
Hexosaminidase A
Hexosaminidase B
Isoenzymes
Isomerases
Racemases and Epimerases
Carbohydrate Epimerases
Oxidoreductases
Alcohol Oxidoreductases
Lactate Dehydrogenases
L-Lactate Dehydrogenase
Transferases
Glycosyltransferases
N-Acetylhexosaminyltransferases
N-Acetylgalactosaminyltransferases
Nitrogenous Group Transferases
Transaminases
Aspartate Aminotransferases
Phosphotransferases
Phosphotransferases (Alcohol Group Acceptor)
Pyruvate Kinase
Carbohydrates
Amino Sugars
Hexosamines
Galactosamine
Neuraminic Acids
Sialic Acids
Glycoconjugates
Glycolipids
Glycosphingolipids
Acidic Glycosphingolipids
Gangliosides
G(M2) Ganglioside
Neutral Glycosphingolipids
Ceramides
Monosaccharides
Hexoses
Mannose
Imino Sugars
Imino Pyranoses
1-Deoxynojirimycin
Polysaccharides
Glycosaminoglycans
Oligosaccharides
Sugar Acids
Neuraminic Acids
Sialic Acids
Uronic Acids
Lipids
Glycolipids
Glycosphingolipids
Acidic Glycosphingolipids
Gangliosides
G(M2) Ganglioside
Neutral Glycosphingolipids
Ceramides
Membrane Lipids
Phospholipids
Sphingolipids
Glycosphingolipids
Acidic Glycosphingolipids
Gangliosides
G(M2) Ganglioside
Neutral Glycosphingolipids
Ceramides
Sterols
Cholesterol
Phospholipids
Sphingolipids
Sterols
Cholesterol
Amino Acids, Peptides, and Proteins
Amino Acids
Amino Acids, Basic
Arginine
Glutamine
Amino Acids, Diamino
Arginine
Glutamine
Amino Acids, Essential
Arginine
Amino Acids, Neutral
Glutamine
Proteins
Blood Proteins
Immunoproteins
Immunoglobulins
Antibodies
Autoantibodies
Immunoglobulin Isotypes
Immunoglobulin G
Serum Globulins
Immunoglobulins
Antibodies
Autoantibodies
Immunoglobulin Isotypes
Immunoglobulin G
Globulins
Serum Globulins
Immunoglobulins
Antibodies
Autoantibodies
Immunoglobulin Isotypes
Immunoglobulin G
Protein Isoforms
Isoenzymes
Nucleic Acids, Nucleotides, and Nucleosides
Nucleic Acids
DNA
RNA
RNA, Messenger
Biological Factors
Antigens
Epitopes
Biomedical and Dental Materials
Polymers
Polyethylene Glycols
Chemical Actions and Uses
Pharmacologic Actions
Molecular Mechanisms of Pharmacological Action
Enzyme Inhibitors
Protease Inhibitors
Angiotensin-Converting Enzyme Inhibitors
Physiological Effects of Drugs
Natriuretic Agents
Diuretics
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